#monomac - Twitter Hashtag

6 months ago

ギリギリで間に合って完成！ヌメ革の選択はdelifeさんの製品を触ってみてリスペクト。表紙:「居皮屋」浅原皮漉所中紙:紙のYamari(上質紙) 製本:「かみのみ」イフ【仕様】 A5サイズいい味が出てきたころに使い切ってしまいそう。中紙が交換できないことか… #モノマチ #モノマチ2026 #monomac

Noosu's tweet photo. ギリギリで間に合って完成！ヌメ革の選択はdelifeさんの製品を触ってみてリスペクト。

表紙:「居皮屋」浅原皮漉所
中紙:紙のYamari(上質紙)
製本:「かみのみ」イフ
【仕様】
A5サイズ

いい味が出てきたころに使い切ってしまいそう。中紙が交換できないことか…
#モノマチ #モノマチ2026 #monomac https://t.co/FRaKAoA3SB

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noosu/ノオス @Noosu

6 months ago

@monomachi2026 カッコいいのにもったいない！もっと打ち出した方がいい！ #モノマチ #モノマチ2026 #monomac

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Satya Prakash Yadav @Satyayadav__

almost 3 years ago

@TheEBMT @ASTCT @ASPHO_hq @pho_india @iapindia @nihardesai7 @DrManasKalra1 @JJ_boelens @AkshaySharmaMD @NicoGagelmann @akshatdoctor @ASH_hematology 1/14 #GATA2 insufficiency is another cause of neutropenia It’s can cause #Emberger syndrome - deafness, lymphadenopathy, #MDS #Monomac syndrome is another presentation Aplastic anemia /recurrent infections /leukemia also part of spectrum Allo BMT is curative

Satyayadav__'s tweet photo. @TheEBMT @ASTCT @ASPHO_hq @pho_india @iapindia @nihardesai7 @DrManasKalra1 @JJ_boelens @AkshaySharmaMD @NicoGagelmann @akshatdoctor @ASH_hematology 1/14

#GATA2 insufficiency is another cause of neutropenia

It’s can cause #Emberger syndrome - deafness, lymphadenopathy, #MDS

#Monomac syndrome is another presentation

Aplastic anemia /recurrent infections /leukemia also part of spectrum

Allo BMT is curative https://t.co/plTFWOVg26

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Satya Prakash Yadav @Satyayadav__

almost 3 years ago

Successful Nonmyeloablative Allogeneic Stem Cell Transplant in a Child With Emberger Syndrome and GATA2 Mutation #GATA2 #MDS #MonoMac https://t.co/4hpceiDLdy

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Mayo Clinic Infectious Diseases

@MayoClinicINFD

over 4 years ago

4/ Depending on #GATA2 gene mutation, it can lead to different syndromic phenotypes such as: #Monocytopenia and #Mycobacterium Avium Complex (#MonoMAC) syndrome https://t.co/lUpdhlYBsX

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Yazan Samhouri MD @yazansamhouri

almost 6 years ago

#GATA2 encodes a zinc finger transcription factor that is required for hematopoiesis. Its def causes multiple clinical syndromes, one is "#MonoMAC" syndrome; monocytopenia and mycobacterial (non-TB) infections. Inheritance is autosomal dominant. @ASH_hematology

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